Abstract

Extraosseous Ewing’s sarcoma also referred to as Extraskeletal Ewing’s sarcoma is a rare tumor of primitive cells which occurs in children, adolescents and young adults. This tumor mainly involves the soft tissue of the extremities and thorax. We report a case of Extraskeletal Ewing’s sarcoma of jejunum without associated skeletal location. A 22 year old female presented with complaints of pain abdomen and vomiting for two days. CT report was leiomyosarcoma /GIST arising from one of the distal jejunal loops. After surgery the specimen was sent to the pathology department. We received 35cm long intestinal segment showing 10x8x6cm grey brown nodular mass, which on cut section extending into the luminal aspect of small intestine. On histopathological examination it was reported as small round cell tumor. The tumor is immunoreactive for CD99 & S100 protein and immunonegative for CD45. Based on these features it was reported as Extraskeletal Ewing’s sarcoma.