Abstract

Darier’s disease (DD) or Keratosis follicularis is a rare cutaneous disease with an autosomal dominant mode of inheritance. It was first described by Darier and White in 1989. It manifests as hyperkeratotic papules, primarily affecting seborrheic areas on the head, neck, and thorax. Histologically, the lesions present as suprabasal clefts in the epidermis with acantholytic and dyskeratotic cells which are represented by corps ronds and grains. Oral retinoid is the treatment of choice for severe disease. Herein we present a series of three cases of Darier’s disease with clinical and histopathological correlation